Paraganglioma of external auditory canal: A rare entity Renu S Rajguru, Shruti Anil Sharma, Ritu K Mehta, Inderdeep Singh Indian Journal of Otology 2019 25(1):34-36 We present the description of a painful paraganglioma of the external auditory canal. Atypical presentation made the diagnosis difficult. We discuss the role of histopathology and immunohistochemistry in the diagnosis of the condition. A 43-year-old male presented with left-sided otalgia and hearing loss. Physical examination revealed a firm swelling arising from the posterosuperior portion of the left external auditory canal. Differential diagnosis of exostosis and squamous cell carcinoma of the external auditory canal was considered. The high-resolution computed tomography of the temporal bones was suggestive of neoplasia. The patient underwent excision biopsy. The hemorrhage during surgery led to suspicion of a vascular tumour. The histopathology and immunohistochemistry confirmed the diagnosis of paraganglioma. Early intervention with imaging and biopsy should be sought for unusual masses of the external ear.